Gyriform calcifications in tuberous sclerosis simulating the appearance of Sturge-Weber disease.
نویسندگان
چکیده
Two cases of tuberous sclerosis are presented. Extensive superficial occipital calcifications were found as classically described in Sturge-Weber syndrome. Other radiologic signs of tuberous sclerosis, such as subependymal calcifications in both patients and surgically proved giant cell astrocytoma in one patient, were present. At pathologic examination, the calcifications appeared to be located in extensive cortical tubers.
منابع مشابه
Sturge-Weber syndrome with extensive intracranial calcifications contralateral to the bulk of the facial nevus, normal intelligence, and absent seizure disorder.
Sturge-Weber syndrome is a rare condition first described by Sturge in 1879 in a case report of an epileptic patient [1] . The association of intracranial calcifications was subsequently described by Weber in 1922, giving this condition its familiar eponym [2] . The classical findings include gyriform intracranial calcifications, congenital and usually unilateral capillary facial nevus, convuls...
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ورودعنوان ژورنال:
- AJNR. American journal of neuroradiology
دوره 13 1 شماره
صفحات -
تاریخ انتشار 1992